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Perioperative Management Of Argininemia Child Undergoing Circumcision: A Case Report

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dc.contributor.authorSuki Ismet
dc.contributor.authorMuhamad Rafiqi Hehsan
dc.date.accessioned2024-10-20T17:04:32Z
dc.date.available2024-10-20T17:04:32Z
dc.date.issued2024
dc.date.submitted2024-10-18
dc.descriptionJournal of PeriAnesthesia Nursing
dc.description.abstractArgininemia is a rare autosomal recessive metabolic disorder characterized by a deficiency of arginase, a vital enzyme in the urea cycle. This metabolic defect results in the accumulation of arginine and its metabolites, leading to hyperammonemia and associated neurological symptoms. We present a case detailing the perioperative management of an 11-year-old male child diagnosed with argininemia undergoing circumcision. The perioperative management of patients with argininemia presents unique challenges due to the risk of hyperammonemia and neurological decompensation triggered by physiological stress, fasting, and the catabolic state associated with surgery. This case report highlights the importance of individualized anesthetic strategies for patients with rare metabolic disorders like argininemia. A multidisciplinary approach involving collaboration among anesthesiologists, endocrinologists, dietitians, and surgeons is essential to ensuring a safe perioperative experience for these patients. Further research is essential to refine perioperative protocols and optimal anesthetic interventions for individuals with argininemia undergoing surgical procedures.
dc.identifier.citationSuki Ismet, Muhamad Rafiqi Hehsan (2024). Perioperative Management of Argininemia Child Undergoing Circumcision: A Case Report. Journal of PeriAnesthesia Nursing. https://doi.org/10.1016/j.jopan.2024.05.025
dc.identifier.doi10.1016/j.jopan.2024.05.025
dc.identifier.epage3
dc.identifier.issn1089-9472
dc.identifier.issue-
dc.identifier.other2208-31
dc.identifier.spage1
dc.identifier.urihttps://oarep.usim.edu.my/handle/123456789/23760
dc.identifier.volume-
dc.language.isoen_US
dc.publisherElsevier Inc.
dc.relation.ispartofJournal of PeriAnesthesia Nursing
dc.relation.issn1532-847
dc.relation.journalJournal of PeriAnesthesia Nursing
dc.subjectarginase deficiency
dc.subjectcase report
dc.subjecthyperammonemia
dc.subjectperioperative
dc.subjecturea cycle disorder
dc.titlePerioperative Management Of Argininemia Child Undergoing Circumcision: A Case Report
dc.typetext::journal::journal article::research article
dspace.entity.typePublication
oairecerif.author.affiliation#PLACEHOLDER_PARENT_METADATA_VALUE#
oairecerif.author.affiliationUniversiti Sains Islam Malaysia

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